Dermatofibrosarcoma protuberans : Reports of 5 cases.

Dermatofibrosarcoma protuberans.

Overview The NCCN Non-Melanoma Skin Cancer Panel has developed these guidelines outlining the treatment of dermatofibrosarcoma protuberans (DFSP) to supplement their other guidelines (NCCN Clinical Practice Guidelines in Oncology [NCCN Guidelines] for Basal Cell and Squamous Cell Skin Cancers and Merkel Cell Carcinoma; to view the most recent version of these guidelines, visit the NCCN Web site...

Transformed dermatofibrosarcoma protuberans: a clinicopathological study of eight cases.

BACKGROUND Fibrosarcomatous (FS) or malignant fibrous histiocytomatous (MFH) transformation of dermatofibrosarcoma protuberans (DFSP) is a rare, but well known, entity. DFSPs with sarcomatous areas have questionable biological behaviour. Several studies suggest that they have a higher risk for local recurrence and distant metastases than ordinary DFSPs. One recent study described no difference ...

DermatoFibrosarcoma Protuberans - A rare dermatologic malignancy: 120 case reports

Background: The dermatofibrosarcoma protuberans is a rare skin tumor with a low grade malignancy. It is characterized by a random and asymmetric local extension and a spontaneous tendency to local recurrence. This characteristic is the main difficulty in the management of dermatofibrosarcoma protuberans. The aim of our study was to evaluate our experience in the management of this disease and t...

Dermatofibrosarcoma Protuberans in Childhood

Dermatofibrosarcoma protuberans in childhood.

Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous tumor with a possibly misleading presentation. It is rare in childhood. We report an 18-month-old child with an acquired atrophic plaque of the left ankle. Based on clinical findings, initial proposed diagnoses included localized scleroderma and localized lipoatrophy. At the age of 5 years the plaque had increased in size and become a p...